Minimal requirements for the elective “Genetics of Endocrine Diseases”

Compiled by Prof. Dr. Igaz Péter

Neptune code: AOSEDT869_1A

 

Main forms of genetics based endocrine diseases

Definition of genetic counseling

Levels of prevention of genetic diseases

Monogenic inheritance patterns (autosomal dominant and recessive, X-linked dominant and recessive)

Definition of penetrance

Definition of genomic imprinting and its endocrinological relevance

Main features of multiple endocrine neoplasia syndromes

Multiple endocrine neoplasia type 1 – main forms and genetics

Multiple endocrine neoplasia type 2 – main forms and genetics

von Hippel-Lindau syndrome – main forms, pathogenesis, genetics

Hereditary paraganglioma syndromes -main forms, genetics

Genetics of pituitary tumors

Genetics of hypopituitarism (maini transcription factors)

Monogenic diseases predisposing to adrenocortical cancer (Li-Fraumeni, Beckwith-Wiedemann syndrome)

Genetics of McCune-Albright syndrome

Main features of pheochromocytoma/paraganglioma genetics

Genetics of differentiated thyroid cancer

Genetics of congenital adrenal hyperplasia (21 hydroxylase deficiency), forms, clinical picture

Genetics of primary aldosteronism, familial hyperaldosteronism type 1

Sex chromosome abnormalities (Klinefelter-syndrome, Turner-syndrome) genetics and clinical features

Prader-Willi syndrome: genetics and clinical features

Genetics of  phenylketonuria

Genetics of monogenic diabetes mellitus (MODY forms)