{"id":185,"date":"2016-01-08T00:00:00","date_gmt":"2016-01-07T23:00:00","guid":{"rendered":"http:\/\/semmelweis.hu\/kutlab\/122-32432\/"},"modified":"2023-07-28T11:25:16","modified_gmt":"2023-07-28T09:25:16","slug":"122-32432","status":"publish","type":"page","link":"https:\/\/semmelweis.hu\/kutlab\/betegellatas\/hemolitikus-uremia\/husrol-orvosoknak\/122-32432\/","title":{"rendered":"A HUS kivizsg\u00e1l\u00e1s sor\u00e1n v\u00e9gzett m\u00e9r\u00e9sek \u00e9rt\u00e9kel\u00e9se"},"content":{"rendered":"<p><span style=\"color: #000000; font-family: Times New Roman; font-size: medium;\"><strong>At\u00edpusos HUS<\/strong> megfelel\u0151 klinikai k\u00e9p (relapszus) vagy pozit\u00edv sz\u00f6vettani lelet kimondhat\u00f3 akkor is, ha a komplementparam\u00e9terek k\u00f6z\u00f6tt nem mutathat\u00f3 ki k\u00f3ros elt\u00e9r\u00e9s. A leggyakrabban l\u00e1tott komplement elt\u00e9r\u00e9s a C3 cs\u00f6kkent szintje (&lt;0,7 g\/L) \u00e9s az alternat\u00edv reakci\u00f3\u00fat cs\u00f6kkent (&lt;70%) aktivit\u00e1sa. Sz\u00e1mos m\u00e1s regul\u00e1tor szintj\u00e9ben is mutatkozhat elt\u00e9r\u00e9s (cs\u00f6kkent H-, B- vagy I-faktor szint), ami al\u00e1t\u00e1masztja a diagn\u00f3zist. Autoimmun eredet\u0171 aHUS anti-H-faktor autoantitestek eset\u00e9n mondhat\u00f3 ki, ilyenkor gyakran \u00e9szlelehet\u0151 elt\u00e9r\u00e9s a komplement regul\u00e1torok szintj\u00e9ben is. <\/span><\/p>\n<p><span style=\"color: #000000; font-family: Times New Roman; font-size: medium;\"><strong>D+HUS<\/strong> eset\u00e9n egyes korai esetekben pozit\u00edv lehet az IgM anti-O157 LPS (enteropatog\u00e9n<em> E. coli<\/em> t\u00f6rzs specifikus antig\u00e9nje) vizsg\u00e1lat, de m\u00e1s esetekben minden vizsg\u00e1lati eredm\u00e9ny negat\u00edv. <\/span><\/p>\n<p><span style=\"font-size: medium;\"><span style=\"color: #000000;\"><span style=\"font-family: Times New Roman;\">Az igazolt <strong>P-HUS<\/strong> esetekben eddig minden alkalommal pozit\u00edv eredm\u00e9nyt adott a neuraminid\u00e1z aktivit\u00e1s\u00e1nak meghat\u00e1roz\u00e1sa az \u00e1ltalunk l\u00e1tott betegekben. <b><\/b><\/span><\/span><\/span><\/p>\n","protected":false},"excerpt":{"rendered":"<p>At\u00edpusos HUS megfelel\u0151 klinikai k\u00e9p (relapszus) vagy pozit\u00edv sz\u00f6vettani lelet kimondhat\u00f3 akkor is, ha a komplementparam\u00e9terek k\u00f6z\u00f6tt nem mutathat\u00f3 ki k\u00f3ros elt\u00e9r\u00e9s. A leggyakrabban l\u00e1tott komplement elt\u00e9r\u00e9s a C3 cs\u00f6kkent szintje (&lt;0,7 g\/L) \u00e9s az alternat\u00edv reakci\u00f3\u00fat cs\u00f6kkent (&lt;70%) aktivit\u00e1sa. Sz\u00e1mos m\u00e1s regul\u00e1tor szintj\u00e9ben is mutatkozhat elt\u00e9r\u00e9s (cs\u00f6kkent H-, B- vagy I-faktor szint), ami al\u00e1t\u00e1masztja &hellip;<\/p>\n","protected":false},"author":1,"featured_media":0,"parent":150,"menu_order":3,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_acf_changed":false,"footnotes":""},"categories":[],"tags":[],"class_list":["post-185","page","type-page","status-publish","hentry"],"acf":[],"_links":{"self":[{"href":"https:\/\/semmelweis.hu\/kutlab\/wp-json\/wp\/v2\/pages\/185","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/semmelweis.hu\/kutlab\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/semmelweis.hu\/kutlab\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/semmelweis.hu\/kutlab\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/semmelweis.hu\/kutlab\/wp-json\/wp\/v2\/comments?post=185"}],"version-history":[{"count":2,"href":"https:\/\/semmelweis.hu\/kutlab\/wp-json\/wp\/v2\/pages\/185\/revisions"}],"predecessor-version":[{"id":1717,"href":"https:\/\/semmelweis.hu\/kutlab\/wp-json\/wp\/v2\/pages\/185\/revisions\/1717"}],"up":[{"embeddable":true,"href":"https:\/\/semmelweis.hu\/kutlab\/wp-json\/wp\/v2\/pages\/150"}],"wp:attachment":[{"href":"https:\/\/semmelweis.hu\/kutlab\/wp-json\/wp\/v2\/media?parent=185"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/semmelweis.hu\/kutlab\/wp-json\/wp\/v2\/categories?post=185"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/semmelweis.hu\/kutlab\/wp-json\/wp\/v2\/tags?post=185"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}